Rodríguez Morata, AlejandroHidalgo Conde, AnaCruz Cosme, Carlos de laGómez Ramírez, SusanaGómez Medialdea, Rafael2013-03-202013-03-202012-11Rodríguez Morata A, Hidalgo Conde A, Cruz Cosme C de la, Gómez Ramírez S, Gómez Medialdea R. Atypical Vascular Involvement in a Case of Behçet's Disease. Case Rep Surg; 2012:8481012090-6900http://hdl.handle.net/10668/863Journal Article;Introduction. Behçet's disease (BD) is a form of vasculitis of unknown etiology which is rare in our environment. It is characterized by a variety of clinical manifestations and usually affects young adults. Recurrent oral and genital ulcers are a characteristic and extremely frequent symptom, but mortality is linked with more significant symptoms such as aortic pseudoaneurysm, pulmonary pseudoaneurysm, and cerebral venous thrombosis. Patient and Method. We present a case of a young male with atypical BD and severe polyvascular involvement (previous cerebral venous thrombosis and current peripheral venous thrombosis, acute ischemia, and peripheral arterial pseudoaneurysm) who required urgent surgical intervention due to a symptomatic external iliac pseudoaneurysm. Result. The pseudoaneurysm was successfully treated, we performed an iliofemoral bypass, and we treated it with steroids and immunosuppressive therapy. Conclusions. These rare clinical manifestations highlight the importance of considering BD in young patients, even in usual cases of vascular intervention, whether arterial or venous in nature.enSíndrome de BehçetAneurisma FalsoEnfermedades VascularesHumanosMedical Subject Headings::Diseases::Skin and Connective Tissue Diseases::Skin Diseases::Skin Diseases, Vascular::Behcet SyndromeMedical Subject Headings::Diseases::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, FalseMedical Subject Headings::Diseases::Cardiovascular Diseases::Vascular DiseasesMedical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::HumansMedical Subject Headings::Named Groups::Persons::Age Groups::Adult::Middle AgedMedical Subject Headings::Diseases::Cardiovascular Diseases::Vascular Diseases::Arterial Occlusive DiseasesMedical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Surgical Procedures, Operative::Cardiovascular Surgical Procedures::Vascular Surgical Procedures::Vascular GraftingAtypical Vascular Involvement in a Case of Behçet's Disease.research article23227411open access10.1155/2012/8481012090-6919PMC3514815