Oliver, Jose MariaGallego, PastoraGonzalez, Ana ElviraGarcia-Hamilton, DiegoAvila, PabloYotti, RaquelFerreira, IgnacioFernandez-Aviles, Francisco2023-02-122023-02-122017-04-210195-668Xhttp://hdl.handle.net/10668/18948AimsTo examine factors related to excess mortality in a cohort of adults with congenital heart disease (CHD).Methods and resultsWe conducted a survival analysis using prospective data of 3311 adults with CHD [ 50.5% males, median age at entry 22.5 years (IQR 18-39), median follow-up time 10.5 years (IQR: 4.4-18)]. Survival status of each patient was further verified by cross checking with the Spanish National Death Index. During a total follow-up of 37608 person-years, 336 (10%) patients died. Annual death rate was 0.89% and standardized mortality ratio (SMR) 2.64 [95% confidence interval (CI) 2.3-3.0; PenAdult congenital heart diseaseHeart defectsCongenitalFollow-up studiesExcess mortalityRisk factors for deathPediatric cardiac-surgeryFollow-upSurvival prospectsUnited-statesPopulationMortalityTrendsDeathDefectsAgeRisk factors for excessmortality in adults with congenital heart diseasesresearch articleopen access10.1093/eurheartj/ehw5901522-9645https://academic.oup.com/eurheartj/article-pdf/38/16/1233/13703161/ehw590.pdf400278800016