Happle, RudolfMetze, DieterVera Casaño, Ángel2012-05-072012-05-072010-03Happle R, Metze D, Vera Casaño A. Naevus lentiginosus linearis: A distinct skin disorder. Acta Derm Venereol. 2010;90(2):210-1.1651-2057http://hdl.handle.net/10668/393Comment in Acta Derm Venereol. 2011 Mar;91(2):209; author reply 209.Congenital naevi of the melanocytic system include numerous types, which differ in their clinical appearance, pattern of distribution, and histopathological features (1). Examples are large congenital melanocytic naevus, macular naevus spilus, papular naevus spilus, café-au-lait macules of neurofibromatosis 1, café-au-lait macules arranged in broad bands as noted in McCune-Albright syndrome, partial unilateral lentiginosis, naevus achromicus (naevus depigmentosus), phylloid hypermelanosis, and phylloid hypomelanosis (1–3). We describe here two patients with a systematized pigmentary naevus that differed from all naevi reported so far.enNevoNeoplasias cutáneasTerminología como AsuntoBiopsiaMedical Subject Headings::Diseases::Skin and Connective Tissue Diseases::Skin Diseases::Pigmentation Disorders::Hyperpigmentation::Melanosis::LentigoMedical Subject Headings::Diseases::Neoplasms::Neoplasms by Histologic Type::Nevi and Melanomas::Nevus::Nevus, PigmentedMedical Subject Headings::Diseases::Neoplasms::Neoplasms by Site::Skin NeoplasmsMedical Subject Headings::Information Science::Information Science::Communication::Language::Linguistics::Terminology as TopicMedical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Diagnosis::Diagnostic Techniques and Procedures::Diagnostic Techniques, Surgical::BiopsyNaevus Lentiginosus Linearis: A Distinct Skin Disorderletter20169318open access10.2340/00015555-08100001-5555