TY - JOUR AU - Rodriguez-Gonzalez, Moises AU - Lubian-Gutierrez, Manuel AU - Cascales-Poyatos, Helena Maria AU - Perez-Reviriego, Alvaro Antonio AU - Castellano-Martinez, Ana PY - 2020 DO - 10.3390/ijms22010356 SN - 1661-6596 UR - http://hdl.handle.net/10668/4289 T2 - International Journal of Molecular Sciences AB - Dystrophin-deficient cardiomyopathy (DDC) is currently the leading cause of death in patients with dystrophinopathies. Targeting myocardial fibrosis (MF) has become a major therapeutic goal in order to prevent the occurrence of DDC. We aimed to review... LA - en PB - MDPI KW - Dystrohinopathy KW - Duchenne muscular disease KW - Becker muscular disease KW - Dystrophic deficient cardiomyopathy KW - Cardiac fibrosis KW - Renin angiotensin system KW - Angiotensin 2 KW - Angiotensin converter enzyme inhibitors KW - Angiotensin receptor blockers KW - Enfermedades musculares KW - Distrofia muscular de Duchenne KW - Cardiomiopatías KW - Distrofias musculares KW - Fibrosis KW - Sistema renina-angiotensina KW - Angiotensina II KW - Inhibidores de la enzima convertidora de angiotensina KW - Antagonistas de receptores de angiotensina KW - Medical Subject Headings::Organisms::Eukaryota::Animals KW - Medical Subject Headings::Diseases::Cardiovascular Diseases::Heart Diseases::Cardiomyopathies KW - Medical Subject Headings::Chemicals and Drugs::Amino Acids, Peptides, and Proteins::Proteins::Contractile Proteins::Muscle Proteins::Dystrophin KW - Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans KW - Medical Subject Headings::Phenomena and Processes::Metabolic Phenomena::Metabolism::Renin-Angiotensin System KW - Medical Subject Headings::Chemicals and Drugs::Chemical Actions and Uses::Pharmacologic Actions::Molecular Mechanisms of Pharmacological Action::Angiotensin Receptor Antagonists KW - Medical Subject Headings::Chemicals and Drugs::Chemical Actions and Uses::Pharmacologic Actions::Molecular Mechanisms of Pharmacological Action::Enzyme Inhibitors::Protease Inhibitors::Angiotensin-Converting Enzyme Inhibitors KW - Medical Subject Headings::Chemicals and Drugs::Hormones, Hormone Substitutes, and Hormone Antagonists::Hormone Antagonists::Mineralocorticoid Receptor Antagonists KW - Medical Subject Headings::Chemicals and Drugs::Hormones, Hormone Substitutes, and Hormone Antagonists::Hormones::Peptide Hormones::Angiotensins::Angiotensin II KW - Medical Subject Headings::Chemicals and Drugs::Amino Acids, Peptides, and Proteins::Proteins::Membrane Proteins::Dystrophin TI - Role of the Renin-Angiotensin-Aldosterone System in Dystrophin-Deficient Cardiomyopathy TY - review article ER -