RT Journal Article
T1 Idiopathic pleuroparenchymal fibroelastosis, a new idiopathic interstitial pneumonia: A case report.
A1 Soto-Hurtado, Enrique Javier
A1 Amaya-Gonzalez, Maria Luisa
A1 Soto, Maria Del Mar Elena
A1 Cabello-Rueda, Francisco Jose
A1 Perez-Nadal, Francisco Javier
A1 Ruiz-Cantero, Alberto
K1 Idiopathic pleuroparenchymal fibroelastosis
K1 Idiopathic interstitial pneumonia
K1 Pleural fibrosis
K1 Pleuroparenchymal fibroelastosis
K1 Pulmonary fibrosis
K1 Área de Gestión Sanitaria Serrania de Malaga
AB Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare disease, idiopathic in most of the cases described in the literature. We report the case of a 55-year-old patient, non-smoker with tuberculosis treated in his youth, starting with progressive dyspnoea and cough, with radiographic abnormalities consisting of pleural thickening, bronchiectasis and structural distortion predominantly in the upper lobes. Due to functional impairment and persistent radiographic abnormalities, biopsy by video-assisted thoracoscopic surgical was decided. The presence of striking elastosis, absence of interstitial damage and abrupt boundary of the fibrous lesion with healthy lung allowed the diagnosis of IPPFE. Currently, the patient has no specific treatment and is in follow-up in the Transplant Unit.
PB Sage Publications
YR 2016
FD 2016-01-25
LK http://hdl.handle.net/10668/9774
UL http://hdl.handle.net/10668/9774
LA en
NO Hurtado EJ, González ML, Soto Mdel M, Rueda FJ, Nadal FJ, Cantero AR. Idiopathic pleuroparenchymal fibroelastosis, a new idiopathic interstitial pneumonia: A case report. Chron Respir Dis. 2016 Aug;13(3):312-6
DS RISalud
RD Apr 12, 2025