RT Journal Article
T1 [Leiomyosarcoma of the inferior vena cava. Case report and literature review].
T2 Leiomiosarcoma de vena cava inferior. Caso clínico y revisión bibliográfica.
A1 López-Ruiz, José Antonio
A1 Tallón-Aguilar, Luis
A1 Marenco-de la Cuadra, Beatriz
A1 López-Pérez, José
A1 Oliva-Mompeán, Fernando
A1 Padillo-Ruiz, Javier
K1 Inferior vena cava
K1 Leiomiosarcoma
K1 Leiomyosarcoma
K1 Neoplasia de tejidos blandos
K1 Soft tissue neoplasm
K1 Vena cava inferior
AB Large vessel sarcomas are rare tumours. Leiomyosarcoma of the inferior vena cava is the most common. About 300 cases have been reported in the literature. They tend to be large, and not develop metastasis. The prognosis of these tumours is poor. An 81 year-old woman who complained of pain in the right flank, with no other symptoms. Abdominal computed tomography showed a large retroperitoneal mass, which affected the inferior vena cava, with signs of thrombosis inside. It also encompassed the right renal vein and the right kidney. Excision of the tumour was performed in block, performing an autologous saphenous vein bypass between left the renal vein and proximal segment of inferior vena cava. Leiomyosarcomas of the inferior vena cava are classified according to their relationship with adjacent structures. The clinical signs and symptoms are generally non-specific. Diagnosis is made using computed tomography or magnetic resonance imaging, and biopsy of the retroperitoneal mass. Surgery is the only treatment capable of providing prolonged survival. The surgical management is determined by: the level of involvement, the extension, and the presence or absence of collateral veins. The role of adjuvant therapy is controversial. Inferior vena cava leiomyosarcomas remain a challenge for surgeons. At present, radical resection with negative margins, offers the highest survival rate. The best results are obtained with a multidisciplinary approach by experienced teams in the management of these tumours.
YR 2016
FD 2016-06-16
LK http://hdl.handle.net/10668/10189
UL http://hdl.handle.net/10668/10189
LA es
DS RISalud
RD Apr 9, 2025