RT Journal Article T1 Temporal bone and intracranial abnormalities in syndromic causes of hearing loss: an updated guide. A1 D'Arco, Felice A1 Youssef, Adam A1 Ioannidou, Evangelia A1 Bisdas, Sotirios A1 Pinelli, Lorenzo A1 Caro-Dominguez, Pablo A1 Nash, Robert A1 Siddiqui, Ata A1 Talenti, Giacomo K1 Brain malformations K1 Head and neck radiology K1 Inner ear malformations K1 Pediatric radiology K1 Syndromic hearing loss AB To describe in detail the temporal bone and brain findings in both common and rare syndromic causes of hearing loss, with the purpose of broadening among radiologists and enhance the current understanding of distinct imaging features in paediatric patients with syndromic hearing loss. A detailed search of electronic databases has been conducted, including PubMed, Ovid Medline, Scopus, Cochrane Library, Google Scholar, National Institute for Health and Care Excellence (NICE), Embase, and PsycINFO. Syndromic causes of hearing loss are characterised by different and sometimes specific abnormalities in the temporal bone. A complete knowledge of the image findings in the temporal bones, brain, skull and other body regions is critical for the optimal assessment and management of these patients. YR 2019 FD 2019-12-26 LK http://hdl.handle.net/10668/14906 UL http://hdl.handle.net/10668/14906 LA en DS RISalud RD Apr 15, 2025