TY - JOUR AU - Piñol-Jurado, Patricia AU - Suárez-Calvet, Xavier AU - Fernández-Simón, Esther AU - Gallardo, Eduard AU - de la Oliva, Natalia AU - Martínez-Muriana, Anna AU - Gómez-Gálvez, Pedro AU - Escudero, Luis M AU - Pérez-Peiró, María AU - Wollin, Lutz AU - de Luna, Noemi AU - Navarro, Xavier AU - Illa, Isabel AU - Díaz-Manera, Jordi PY - 2018 DO - 10.1038/s41419-018-0792-6 UR - http://hdl.handle.net/10668/12700 T2 - Cell death & disease AB - Duchenne muscle dystrophy (DMD) is a genetic disorder characterized by progressive skeletal muscle weakness. Dystrophin deficiency induces instability of the sarcolemma during muscle contraction that leads to muscle necrosis and replacement of muscle... LA - en KW - Action Potentials KW - Animals KW - Collagen Type I KW - Collagen Type I, alpha 1 Chain KW - Collagen Type III KW - Disease Models, Animal KW - Dystrophin KW - Fibrosis KW - Indoles KW - Male KW - Mice KW - Muscle Contraction KW - Muscle Weakness KW - Muscle, Skeletal KW - Muscular Dystrophy, Duchenne KW - Platelet-Derived Growth Factor KW - Transforming Growth Factor beta1 TI - Nintedanib decreases muscle fibrosis and improves muscle function in a murine model of dystrophinopathy. TY - research article VL - 9 ER -