TY - JOUR AU - El-Sayed, Zeinab A AU - Abramova, Irina AU - Aldave, Juan Carlos AU - Al-Herz, Waleed AU - Bezrodnik, Liliana AU - Boukari, Rachida AU - Bousfiha, Ahmed Aziz AU - Cancrini, Caterina AU - Condino-Neto, Antonio AU - Dbaibo, Ghassan AU - Derfalvi, Beata AU - Dogu, Figen AU - Edgar, J David M AU - Eley, Brian AU - El-Owaidy, Rasha Hasan AU - Espinosa-Padilla, Sara Elva AU - Galal, Nermeen AU - Haerynck, Filomeen AU - Hanna-Wakim, Rima AU - Hossny, Elham AU - Ikinciogullari, Aydan AU - Kamal, Ebtihal AU - Kanegane, Hirokazu AU - Kechout, Nadia AU - Lau, Yu Lung AU - Morio, Tomohiro AU - Moschese, Viviana AU - Neves, Joao Farela AU - Ouederni, Monia AU - Paganelli, Roberto AU - Paris, Kenneth AU - Pignata, Claudio AU - Plebani, Alessandro AU - Qamar, Farah Naz AU - Qureshi, Sonia AU - Radhakrishnan, Nita AU - Rezaei, Nima AU - Rosario, Nelson AU - Routes, John AU - Sanchez, Berta AU - Sediva, Anna AU - Seppanen, Mikko Rj AU - Serrano, Edith Gonzalez AU - Shcherbina, Anna AU - Singh, Surjit AU - Siniah, Sangeetha AU - Spadaro, Guiseppe AU - Tang, Mimi AU - Vinet, Ana Maria AU - Volokha, Alla AU - Sullivan, Kathleen E PY - 2019 DO - 10.1016/j.waojou.2019.100018 SN - 1939-4551 UR - http://hdl.handle.net/10668/13781 T2 - The World Allergy Organization journal AB - X-linked agammaglobulinemia is an inherited immunodeficiency recognized since 1952. In spite of seven decades of experience, there is still a limited understanding of regional differences in presentation and complications. This study was designed by... LA - en KW - Agammaglobulinemia KW - Autoimmunity KW - CLD, Chronic lung disease KW - FH, Family history KW - GI, Gastrointestinal KW - Immunoglobulin KW - Infection KW - JIA, juvenile idiopathic arthritis KW - Outcomes KW - SCIG, Subcutaneous immunoglobulin KW - Therapy KW - VAPP, Vaccine associated paralytic poliomyelitis KW - XLA KW - XLA, X-linked agammaglobulinemia TI - X-linked agammaglobulinemia (XLA):Phenotype, diagnosis, and therapeutic challenges around the world. TY - research article VL - 12 ER -