RT Journal Article
T1 Susac's syndrome: isolated retinal artery occlusion after 10 years of remission.
A1 García-Basterra, Ignacio
A1 Aranda, Isabel Baquero
A1 García-Ben, Antonio
A1 García-Campos, José Manuel
AB Susac's syndrome, or microangiopathy of the retina, inner ear, and brain, is a rare condition characterized by the clinical triad of encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss. The complete triad has been documented in 85% of reported cases. At clinical onset, the most common manifestations are central nervous system symptoms, followed by visual symptoms and hearing disturbances. Although the clinical course of Susac's syndrome is usually self-limiting, fluctuating, and monophasic, clinical polycyclic and chronic courses have also been described. Likewise, recurrences of the full triad after more than 10 years of remission have been reported. We describe a 21-year-old woman who presented with branch retinal artery occlusions and magnetic resonance imaging findings compatible with Susac's syndrome without objective hearing loss. After 10 years of remission, the patient complained of visual field loss due to new retinal ischemia. Neither other symptoms nor neuroimaging or audiometry pathologic findings were found during the clinical course.
YR 2018
FD 2018
LK http://hdl.handle.net/10668/12518
UL http://hdl.handle.net/10668/12518
LA en
DS RISalud
RD Apr 7, 2025