TY  - JOUR
AU  - García-Laorden, M Isabel
AU  - Hernández-Brito, Elisa
AU  - Muñoz-Almagro, Carmen
AU  - Pavlovic-Nesic, Svetlana
AU  - Rúa-Figueroa, Iñigo
AU  - Briones, M Luisa
AU  - Rajas, Olga
AU  - Borderías, Luis
AU  - Payeras, Antoni
AU  - Lorente, Leonardo
AU  - Freixinet, Jordi
AU  - Ferreres, Jose
AU  - Obando, Ignacio
AU  - González-Quevedo, Nereida
AU  - Rodríguez de Castro, Felipe
AU  - Solé-Violán, Jordi
AU  - Rodríguez-Gallego, Carlos
PY  - 2019
DO  - 10.1007/s10875-019-00714-4
UR  - http://hdl.handle.net/10668/14819
T2  - Journal of clinical immunology
AB  - Mannose-binding lectin (MBL)-associated serine protease-2 (MASP-2) is an indispensable enzyme for the activation of the lectin pathway of complement. Its deficiency is classified as a primary immunodeficiency associated to pyogenic bacterial...
LA  - en
KW  - MASP-2
KW  - MBL
KW  - collectin
KW  - complement
KW  - ficolin-3
KW  - lectin pathway
KW  - primary immunodeficiency
KW  - Adult
KW  - Child
KW  - Community-Acquired Infections
KW  - Female
KW  - Genotype
KW  - Humans
KW  - Lectins
KW  - Lupus Erythematosus, Systemic
KW  - Male
KW  - Mannose-Binding Lectin
KW  - Mannose-Binding Protein-Associated Serine Proteases
KW  - Mutation
KW  - Primary Immunodeficiency Diseases
KW  - Signal Transduction
TI  - Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway.
TY  - research article
VL  - 40
ER  -