TY - JOUR AU - González-García, Pilar AU - Barriocanal-Casado, Eliana AU - Díaz-Casado, María Elena AU - López-Herrador, Sergio AU - Hidalgo-Gutiérrez, Agustín AU - López, Luis C PY - 2021 DO - 10.3390/antiox10111687 SN - 2076-3921 UR - https://hdl.handle.net/10668/26975 T2 - Antioxidants (Basel, Switzerland) AB - Coenzyme Q (CoQ) is a vital lipophilic molecule that is endogenously synthesized in the mitochondria of each cell. The CoQ biosynthetic pathway is complex and not completely characterized, and it involves at least thirteen catalytic and regulatory... LA - en KW - bioenergetics KW - mitochondria KW - mitochondrial disease KW - oxidative stress KW - pathomechanisms KW - preclinical models KW - sulfide metabolism KW - therapy TI - Animal Models of Coenzyme Q Deficiency: Mechanistic and Translational Learnings. TY - research article VL - 10 ER -