TY - JOUR AU - Behr, Jürgen AU - Demedts, Maurits AU - Buhl, Roland AU - Costabel, Ulrich AU - Dekhuijzen, Richard P N AU - Jansen, Henk M AU - MacNee, William AU - Thomeer, Michiel AU - Wallaert, Benoit AU - Laurent, Francois AU - Nicholson, Andrew G AU - Verbeken, Eric K AU - Verschakelen, Johny AU - Flower, C D R AU - Petruzzelli, Stefano AU - De Vuyst, Paul AU - van den Bosch, J M M AU - Rodriguez-Becerra, Eulogio AU - Lankhorst, Ida AU - Sardina, Marco AU - Boissard, Gabrielle PY - 2009 DO - 10.1186/1465-9921-10-101 SN - 1465-9921 UR - http://hdl.handle.net/10668/1657 T2 - Respiratory Research AB - BACKGROUNDThe randomized placebo-controlled IFIGENIA-trial demonstrated that therapy with high-dose N-acetylcysteine (NAC) given for one year, added to prednisone and azathioprine, significantly ameliorates (i.e. slows down) disease progression in... LA - en PB - BIOMED CENTRAL LTD KW - Anciano KW - Azatioprina KW - Progresión de la efermedad KW - Método doble ciego KW - Quimioterapia combinada KW - Europa (continente) KW - Prueba de esfuerzo KW - Femenino KW - Humanos KW - Pulmón KW - Fibrosis pulmonar Idiopática KW - Mediana edad KW - Pacientes desistentes del Tratamiento KW - Prednisona KW - Fármacos del sistema respiratorio KW - Índice de severidad de la enfermedad KW - Resultado del tratamiento KW - Capacidad vital KW - Acetilcisteína KW - Medical Subject Headings::Named Groups::Persons::Age Groups::Adult::Aged KW - Medical Subject Headings::Chemicals and Drugs::Organic Chemicals::Sulfur Compounds::Thionucleosides::Azathioprine KW - Medical Subject Headings::Diseases::Pathological Conditions, Signs and Symptoms::Pathologic Processes::Disease Attributes::Disease Progression KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Investigative Techniques::Epidemiologic Methods::Epidemiologic Research Design::Double-Blind Method KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Therapeutics::Drug Therapy::Drug Therapy, Combination KW - Medical Subject Headings::Geographicals::Geographic Locations::Europe KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Diagnosis::Diagnostic Techniques and Procedures::Diagnostic Techniques, Cardiovascular::Heart Function Tests::Exercise Test KW - Medical Subject Headings::Check Tags::Female KW - Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans KW - Medical Subject Headings::Diseases::Respiratory Tract Diseases::Lung Diseases::Pulmonary Fibrosis::Idiopathic Pulmonary Fibrosis KW - Medical Subject Headings::Anatomy::Respiratory System::Lung KW - Medical Subject Headings::Named Groups::Persons::Age Groups::Adult::Middle Aged KW - Medical Subject Headings::Named Groups::Persons::Patients::Patient Dropouts KW - Medical Subject Headings::Chemicals and Drugs::Polycyclic Compounds::Steroids::Pregnanes::Pregnadienes::Pregnadienediols::Prednisone KW - Medical Subject Headings::Chemicals and Drugs::Chemical Actions and Uses::Pharmacologic Actions::Therapeutic Uses::Respiratory System Agents KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Investigative Techniques::Epidemiologic Methods::Data Collection::Health Surveys::Health Status Indicators::Severity of Illness Index KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Diagnosis::Prognosis::Treatment Outcome KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Diagnosis::Diagnostic Techniques and Procedures::Diagnostic Techniques, Respiratory System::Respiratory Function Tests::Lung Volume Measurements::Total Lung... KW - Medical Subject Headings::Chemicals and Drugs::Organic Chemicals::Sulfur Compounds::Amino Acids, Sulfur::Cysteine::Acetylcysteine TI - Lung function in idiopathic pulmonary fibrosis--extended analyses of the IFIGENIA trial. TY - research article ER -