TY  - JOUR
AU  - Luna-Sanchez, Marta
AU  - Hidalgo-Gutierrez, Agustín
AU  - Hildebrandt, Tatjana M
AU  - Chaves-Serrano, Julio
AU  - Barriocanal-Casado, Eliana
AU  - Santos-Fandila, Angela
AU  - Romero, Miguel
AU  - Sayed, Ramy Ka
AU  - Duarte, Juan
AU  - Prokisch, Holger
AU  - Schuelke, Markus
AU  - Distelmaier, Felix
AU  - Escames, Germaine
AU  - Acuña-Castroviejo, Dario
AU  - Lopez, Luis C
PY  -  201
DO  - 10.15252/emmm.201606345
UR  - http://hdl.handle.net/10668/10613
T2  - EMBO molecular medicine
AB  - Coenzyme Q (CoQ) is a key component of the mitochondrial respiratory chain, but it also has several other functions in the cellular metabolism. One of them is to function as an electron carrier in the reaction catalyzed by sulfide:quinone...
LA  - en
PB  - EMBO Press
KW  - COX
KW  - SQR
KW  - blood pressure
KW  - glutathione
KW  - mitochondrial disease
KW  - Animals
KW  - Ataxia
KW  - Blood Pressure
KW  - Cells, Cultured
KW  - Cerebrum
KW  - Disease Models, Animal
KW  - Fibroblasts
KW  - Humans
KW  - Mice
KW  - Mitochondria
KW  - Mitochondrial Diseases
KW  - Muscle Weakness
KW  - Oxidation-Reduction
KW  - Quinone Reductases
KW  - Sulfides
KW  - Ubiquinone
TI  - CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndrome.
TY  - research article
VL  - 9
ER  -