RT Journal Article
T1 Surgical excision with left atrial reconstruction of a primary functioning retrocardiac paraganglioma.
A1 González López, María Teresa
A1 González González, Sergio
A1 Sarria García, Esteban
A1 González Romero, Stella
A1 Gutiérrez de Loma, Julio
K1 Paraganglioma
K1 Pheochromocytoma
K1 Cardiac tumor
K1 Left atrium
K1 Cardiopulmonary bypass
K1 Procedimientos quirúrgicos cardíacos
K1 Derivación cardiopulmonar
K1 Catecolaminas
K1 Atrios cardíacos
K1 Neoplasias cardíacas
K1 Procedimientos quirúrgicos reparadores
AB About 2% of all paragangliomas are located in the chest, and a few have been described to be found in the heart. Primary cardiac paragangliomas are extremely uncommon tumors and surgical experience with this neoplasm is limited. Treatment strategies described in the literature have included simple excision, excision with reconstruction, autotransplantation after excision of the tumor and even orthotopic cardiac transplantation, depending on the extent of disease. A primary retrocardiac paraganglioma catecholamine-productive was identified in an asymptomatic 49-year old female associated to familial pheochromocytoma-paraganglioma syndrome caused by germline mutation of the gen which codifies for the subunit B of succinate dehydrogenase enzyme (SDHB). The neoplasm was surgically excised from the posterior surface of the left atrium via median sternotomy using cardiopulmonary bypass. Direct ligation of feeding vessels of the tumor along with left atrial reinforcement using a pericardial patch was performed. The post-operative course was uneventful, with normalization of catecholamine secretion and no recurrence at three-month follow-up. We review the current literature about this exceptional cardiac tumor, pathophysiological conditions and options for surgical management.
PB BioMed Central
YR 2013
FD 2013-01-29
LK http://hdl.handle.net/10668/1437
UL http://hdl.handle.net/10668/1437
LA en
NO González López MT, González González S, Sarria García E, González Romero S, Gutierrez de Loma J. Surgical excision with left atrial reconstruction of a primary functioning retrocardiac paraganglioma. J Cardiothorac Surg. 2013; 8:22
NO Case Reports; Journal Article;
DS RISalud
RD Apr 8, 2025