TY - JOUR AU - Ariceta, Gema AU - Lara, Enrique AU - Camacho, Juan A AU - Oppenheimer, Federico AU - Vara, Julia AU - Santos, Fernando AU - Muñoz, Miguel Angel AU - Cantarell, Carmen AU - Gil Calvo, Marta AU - Romero, Rafael AU - Valenciano, Blanca AU - García-Nieto, Víctor AU - Sanahuja, Maria José AU - Crespo, José AU - Justa, Maria Luisa AU - Urisarri, Adela AU - Bedoya, Rafael AU - Bueno, Alberto AU - Daza, Antonio AU - Bravo, Juan AU - Llamas, Francisco AU - Jiménez Del Cerro, Luis Antonio PY - 2015 DO - 10.1093/ndt/gfu329 SN - 0931-0509 UR - http://hdl.handle.net/10668/2229 T2 - Nephrology, Dialysis, Transplantation : Official Publication of the European Dialysis and Transplant Association - European Renal Association AB - BACKGROUNDCysteamine has improved survival and prognosis in cystinosis. Increasing numbers of patients reach adulthood and face new challenges such as compliance that wanes over time. The aim of this study was to evaluate adherence to cysteamine... LA - en PB - Oxford University Press KW - Adherence KW - Cysteamine KW - Cystinosis KW - Prognosis KW - Transition KW - Absentismo KW - Cisteamina KW - Cistinosis KW - Estudios de seguimiento KW - España KW - Trasplante de riñón KW - Cooperación del paciente KW - Pronóstico KW - Autocuidado KW - Olfato KW - Medical Subject Headings::Psychiatry and Psychology::Psychological Phenomena and Processes::Psychology, Applied::Psychology, Industrial::Absenteeism KW - Medical Subject Headings::Named Groups::Persons::Age Groups::Adolescent KW - Medical Subject Headings::Named Groups::Persons::Age Groups::Adult KW - Medical Subject Headings::Named Groups::Persons::Age Groups::Child KW - Medical Subject Headings::Chemicals and Drugs::Organic Chemicals::Amines::Ethylamines::Mercaptoethylamines::Cysteamine KW - Medical Subject Headings::Diseases::Congenital, Hereditary, and Neonatal Diseases and Abnormalities::Genetic Diseases, Inborn::Metabolism, Inborn Errors::Lysosomal Storage Diseases::Cystinosis KW - Medical Subject Headings::Psychiatry and Psychology::Behavior and Behavior Mechanisms::Emotions KW - Medical Subject Headings::Named Groups::Persons::Parents::Fathers KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics as Topic::Epidemiologic Studies::Cohort Studies::Longitudinal... KW - Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans KW - Medical Subject Headings::Anatomy::Urogenital System::Urinary Tract::Kidney KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Therapeutics::Renal Replacement Therapy::Kidney Transplantation KW - Medical Subject Headings::Check Tags::Male KW - Medical Subject Headings::Named Groups::Persons::Parents::Mothers KW - Medical Subject Headings::Psychiatry and Psychology::Behavior and Behavior Mechanisms::Motivation KW - Medical Subject Headings::Named Groups::Persons::Parents KW - Medical Subject Headings::Psychiatry and Psychology::Behavior and Behavior Mechanisms::Behavior::Health Behavior::Patient Compliance KW - Medical Subject Headings::Named Groups::Persons::Occupational Groups::Health Personnel::Physicians KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Diagnosis::Prognosis KW - Medical Subject Headings::Analytical, Diagnostic and Therapeutic Techniques and Equipment::Therapeutics::Self Care KW - Medical Subject Headings::Phenomena and Processes::Musculoskeletal and Neural Physiological Phenomena::Nervous System Physiological Phenomena::Nervous System Physiological Processes::Sensation::Smell KW - Medical Subject Headings::Geographicals::Geographic Locations::Europe::Spain TI - Cysteamine (Cystagon®) adherence in patients with cystinosis in Spain: successful in children and a challenge in adolescents and adults. TY - research article ER -