%0 Journal Article %A Guillen-Del-Castillo, Alfredo %A Meseguer, Manuel López %A Fonollosa-Pla, Vicent %A Gimenez, Berta Sáez %A Colunga-Argüelles, Dolores %A Revilla-Lopez, Eva %A Rubio-Rivas, Manuel %A Ropero, Maria Jose Cristo %A Argibay, Ana %A Barbera, Joan Albert %A Salas, Xavier Pla %A Meñaca, Amaya Martínez %A Vuelta, Ana Belen Madroñero %A Padron, Antonio Lara %A Comet, Luis Saez %A Morera, Juan Antonio Domingo %A Gonzalez-Echavarri, Cristina %A Mombiela, Teresa %A Ortego-Centeno, Norberto %A Gonzalez, Manuela Marín %A Tolosa-Vilella, Carles %A Blanco, Isabel %A Subias, Pilar Escribano %A Simeon-Aznar, Carmen Pilar %T Impact of interstitial lung disease on the survival of systemic sclerosis with pulmonary arterial hypertension. %D 2022 %U http://hdl.handle.net/10668/19596 %X To assess severity markers and outcomes of patients with systemic sclerosis (SSc) with or without pulmonary arterial hypertension (PAH-SSc/non-PAH-SSc), and the impact of interstitial lung disease (ILD) on PAH-SSc. Non-PAH-SSc patients from the Spanish SSc registry and PAH-SSc patients from the Spanish PAH registry were included. A total of 364 PAH-SSc and 1589 non-PAH-SSc patients were included. PAH-SSc patients had worse NYHA-functional class (NYHA-FC), worse forced vital capacity (FVC) (81.2 ± 20.6% vs 93.6 ± 20.6%, P  %~