TY - JOUR AU - Gonzalez-GarcIa, Pilar AU - Hidalgo-Gutierrez, Agustin AU - Mascaraque, Cristina AU - Barriocanal-Casado, Eliana AU - Bakkali, Mohammed AU - Ziosi, Marcello AU - Abdihankyzy, Ussipbek Botagoz AU - Sanchez-Hernandez, Sabina AU - Escames, Germaine AU - Prokisch, Holger AU - Martin, Francisco AU - Quinzii, Catarina M AU - Lopez, Luis C PY - 2020 DO - 10.1093/hmg/ddaa214 UR - http://hdl.handle.net/10668/16314 T2 - Human molecular genetics AB - Abnormalities of one carbon, glutathione and sulfide metabolisms have recently emerged as novel pathomechanisms in diseases with mitochondrial dysfunction. However, the mechanisms underlying these abnormalities are not clear. Also, we recently showed... LA - en PB - Oxford University Press KW - Animals KW - Ataxia KW - Carbon KW - Electron Transport KW - Electron Transport Complex I KW - Fibroblasts KW - Glutathione KW - Humans KW - Mice KW - Mice, Inbred C57BL KW - Mitochondria KW - Mitochondrial Diseases KW - Muscle Weakness KW - Oxidoreductases Acting on Sulfur Group Donors KW - Skin KW - Sulfides KW - Transcriptome KW - Ubiquinone KW - Vitamins TI - Coenzyme Q10 modulates sulfide metabolism and links the mitochondrial respiratory chain to pathways associated to one carbon metabolism. TY - research article VL - 29 ER -