An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)

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dc.contributor.authorKasper, B.
dc.contributor.authorBaumgarten, C.
dc.contributor.authorGarcia, J.
dc.contributor.authorBonvalot, S.
dc.contributor.authorHaas, R.
dc.contributor.authorHaller, F.
dc.contributor.authorHohenberger, P.
dc.contributor.authorPenel, N.
dc.contributor.authorMessiou, C.
dc.contributor.authorvan der Graaf, W. T.
dc.contributor.authorGronchi, A.
dc.contributor.authorDesmoid Working Grp
dc.contributor.authoraffiliation[Kasper, B.] Heidelberg Univ, Mannheim Univ, Sarcoma Unit, Interdisciplinary Tumor Ctr,Med Ctr, Theodor Kutzer Ufer 1-3, D-68167 Mannheim, Germany
dc.contributor.authoraffiliation[Hohenberger, P.] Heidelberg Univ, Mannheim Univ, Sarcoma Unit, Interdisciplinary Tumor Ctr,Med Ctr, Theodor Kutzer Ufer 1-3, D-68167 Mannheim, Germany
dc.contributor.authoraffiliation[Baumgarten, C.] SPAEN Sarcoma PAtients EuroNet eV, Wolfersheim, Germany
dc.contributor.authoraffiliation[Garcia, J.] SPAEN Sarcoma PAtients EuroNet eV, Wolfersheim, Germany
dc.contributor.authoraffiliation[Bonvalot, S.] PSL Univ, Inst Curie, Dept Surg Oncol, Paris, France
dc.contributor.authoraffiliation[Haas, R.] Antoni van Leeuwenhoek Hosp, Dept Radiotherapy, Netherlands Canc Inst, Amsterdam, Netherlands
dc.contributor.authoraffiliation[Haas, R.] Leiden Univ, Med Ctr, Dept Radiotherapy, Leiden, Netherlands
dc.contributor.authoraffiliation[Haller, F.] Friedrich Alexander Univ Erlangen, Inst Pathol, Erlangen, Germany
dc.contributor.authoraffiliation[Penel, N.] Ctr Oscar Lambret, Dept Med Oncol, Lille, France
dc.contributor.authoraffiliation[Messiou, C.] Royal Marsden Hosp, Dept Radiol, London, England
dc.contributor.authoraffiliation[van der Graaf, W. T.] Inst Canc Res, Div Clin Studies, London, England
dc.contributor.authoraffiliation[Gronchi, A.] Fdn IRCCS Ist Nazl Tumori, Dept Surg, Milan, Italy
dc.date.accessioned2025-01-07T15:37:04Z
dc.date.available2025-01-07T15:37:04Z
dc.date.issued2017-10-01
dc.description.abstractDesmoid-type fibromatosis is a rare and locally aggressive monoclonal, fibroblastic proliferation characterized by a variable and often unpredictable clinical course. Currently, there is no established or evidence-based treatment approach available for this disease. Therefore, in 2015 the European Desmoid Working Group published a position paper giving recommendations on the treatment of this intriguing disease. Here, we present an update of this consensus approach based on professionals' AND patients' expertise following a round table meeting bringing together sarcoma experts from the European Organization for Research and Treatment of Cancer/Soft Tissue and Bone Sarcoma Group with patients and patient advocates from Sarcoma PAtients EuroNet. In this paper, we focus on new findings regarding the prognostic value of mutational analysis in desmoid-type fibromatosis patients and new systemic treatment options.
dc.identifier.doi10.1093/annonc/mdx323
dc.identifier.essn1569-8041
dc.identifier.issn0923-7534
dc.identifier.pmid28961825
dc.identifier.unpaywallURLhttps://academic.oup.com/annonc/article-pdf/28/10/2399/24168780/mdx323.pdf
dc.identifier.urihttps://hdl.handle.net/10668/27274
dc.identifier.wosID411827200013
dc.issue.number10
dc.journal.titleAnnals of oncology
dc.journal.titleabbreviationAnn. oncol.
dc.language.isoen
dc.organizationSAS - Hospital Universitario Virgen del Rocío
dc.page.number2399-2408
dc.publisherOxford univ press
dc.rightsAttribution-NonCommercial 4.0 International
dc.rights.accessRightsopen access
dc.rights.urihttp://creativecommons.org/licenses/by-nc/4.0/
dc.subjectdesmoid
dc.subjectaggressive fibromatosis
dc.subjectEORTC/STBSG
dc.subjectpatient advocacy groups
dc.subjectSPAEN
dc.subjecttreatment algorithm
dc.subjectAdvanced aggressive fibromatosis
dc.subjectPhase-ii trial
dc.subjectSoft-tissue
dc.subjectLocal recurrence
dc.subjectAbdominal-wall
dc.subject1st-line management
dc.subjectSurgical resection
dc.subjectPrognostic-factors
dc.subjectTreatment options
dc.subjectSee policy
dc.titleAn update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
dc.typereview
dc.type.hasVersionVoR
dc.volume.number28
dc.wostypeReview

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