Publication:
Impact of interstitial lung disease on the survival of systemic sclerosis with pulmonary arterial hypertension.

dc.contributor.authorGuillen-Del-Castillo, Alfredo
dc.contributor.authorMeseguer, Manuel López
dc.contributor.authorFonollosa-Pla, Vicent
dc.contributor.authorGimenez, Berta Sáez
dc.contributor.authorColunga-Argüelles, Dolores
dc.contributor.authorRevilla-Lopez, Eva
dc.contributor.authorRubio-Rivas, Manuel
dc.contributor.authorRopero, Maria Jose Cristo
dc.contributor.authorArgibay, Ana
dc.contributor.authorBarbera, Joan Albert
dc.contributor.authorSalas, Xavier Pla
dc.contributor.authorMeñaca, Amaya Martínez
dc.contributor.authorVuelta, Ana Belen Madroñero
dc.contributor.authorPadron, Antonio Lara
dc.contributor.authorComet, Luis Saez
dc.contributor.authorMorera, Juan Antonio Domingo
dc.contributor.authorGonzalez-Echavarri, Cristina
dc.contributor.authorMombiela, Teresa
dc.contributor.authorOrtego-Centeno, Norberto
dc.contributor.authorGonzalez, Manuela Marín
dc.contributor.authorTolosa-Vilella, Carles
dc.contributor.authorBlanco, Isabel
dc.contributor.authorSubias, Pilar Escribano
dc.contributor.authorSimeon-Aznar, Carmen Pilar
dc.contributor.groupRESCLE Consortium
dc.contributor.groupREHAP Consortium
dc.date.accessioned2023-05-03T13:26:42Z
dc.date.available2023-05-03T13:26:42Z
dc.date.issued2022-03-11
dc.description.abstractTo assess severity markers and outcomes of patients with systemic sclerosis (SSc) with or without pulmonary arterial hypertension (PAH-SSc/non-PAH-SSc), and the impact of interstitial lung disease (ILD) on PAH-SSc. Non-PAH-SSc patients from the Spanish SSc registry and PAH-SSc patients from the Spanish PAH registry were included. A total of 364 PAH-SSc and 1589 non-PAH-SSc patients were included. PAH-SSc patients had worse NYHA-functional class (NYHA-FC), worse forced vital capacity (FVC) (81.2 ± 20.6% vs 93.6 ± 20.6%, P 
dc.description.versionSi
dc.identifier.citationGuillén-Del-Castillo A, Meseguer ML, Fonollosa-Pla V, Giménez BS, Colunga-Argüelles D, et al. Impact of interstitial lung disease on the survival of systemic sclerosis with pulmonary arterial hypertension. Sci Rep. 2022 Mar 28;12(1):5289. doi: 10.1038/s41598-022-09353-z. Erratum in: Sci Rep. 2022 Jul 28;12(1):12947.
dc.identifier.doi10.1038/s41598-022-09353-z
dc.identifier.essn2045-2322
dc.identifier.pmcPMC8960788
dc.identifier.pmid35347225
dc.identifier.pubmedURLhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC8960788/pdf
dc.identifier.unpaywallURLhttps://www.nature.com/articles/s41598-022-09353-z.pdf
dc.identifier.urihttp://hdl.handle.net/10668/19596
dc.issue.number1
dc.journal.titleScientific reports
dc.journal.titleabbreviationSci Rep
dc.language.isoen
dc.organizationHospital Universitario San Cecilio
dc.organizationInstituto de Investigación Biosanitaria de Granada (ibs.GRANADA)
dc.page.number11
dc.page.number11
dc.provenanceRealizada la curación de contenido 02/09/2024
dc.publisherNature Publishing Group
dc.pubmedtypeJournal Article
dc.pubmedtypeResearch Support, Non-U.S. Gov't
dc.relation.publisherversionhttps://doi.org/10.1038/s41598-022-09353-z
dc.rightsAttribution 4.0 International
dc.rights.accessRightsopen access
dc.rights.urihttp://creativecommons.org/licenses/by/4.0/
dc.subject.decsEnfermedades pulmonares intersticiales
dc.subject.decsHipertensión arterial pulmonar
dc.subject.decsEsclerodermia sistémica
dc.subject.decsHipertensión pulmonar primaria
dc.subject.decsHipertensión pulmonar
dc.subject.meshFamilial Primary Pulmonary Hypertension
dc.subject.meshHumans
dc.subject.meshHypertension, Pulmonary
dc.subject.meshLung Diseases, Interstitial
dc.subject.meshPulmonary Arterial Hypertension
dc.subject.meshScleroderma, Systemic
dc.titleImpact of interstitial lung disease on the survival of systemic sclerosis with pulmonary arterial hypertension.
dc.typeresearch article
dc.type.hasVersionVoR
dc.volume.number12
dspace.entity.typePublication

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