Publication:
Dietoterapia en paciente con linfangiectasia intestinal primaria y ascitis quilosa de repetición.

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Date

2007-11

Authors

Campos Martín, C
Rabat Restrepo, JM
Sendón Pérez, A
Fernández-Argüelles García, A

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Aula Médica Ediciones
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Abstract

OBJECTIVES Primary intestinal lymphangiectasia is a lymphatic system's disorder, where lymphatic drainage is blockaged. Clinically it produces malabsorption, protein-losing enteropathy, hypogammaglobulin in blood, and several degrees of malnutrition. Its treatment is not easy and includes dietetic-therapy and drugs. MATERIAL AND METHOD A 35-year-old-woman case report is exposed. She has recurrent chylosa ascites, requiring several admissions and evacuatory paracentesis. After food-fat was replaced by medium-chain triacyl-glicerol-enriched diet, a clinical, analytical and anthropometric improvement was demonstrated. CONCLUSIONS The major way of treatment in intestinal lymphangiectasia in this case is the employement of specific-diet and adaptaded-basic-food. It's difficult and high collaboration of the patient is required, being necessary medical revisions during the whole life, due to the not well known evolution of this long-standing disease.

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Case Reports; English Abstract; Journal Article;

MeSH Terms

Medical Subject Headings::Diseases::Digestive System Diseases::Peritoneal Diseases::Chylous Ascites
Medical Subject Headings::Check Tags::Female
Medical Subject Headings::Organisms::Eukaryota::Animals::Chordata::Vertebrates::Mammals::Primates::Haplorhini::Catarrhini::Hominidae::Humans
Medical Subject Headings::Diseases::Hemic and Lymphatic Diseases::Lymphatic Diseases::Lymphangiectasis::Lymphangiectasis, Intestinal
Medical Subject Headings::Diseases::Pathological Conditions, Signs and Symptoms::Pathologic Processes::Disease Attributes::Recurrence
Medical Subject Headings::Named Groups::Persons::Age Groups::Adult

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Keywords

Linfangiectasia, Dietoterapia, MCT, Ascitis quilosa, Lymphangiectasia, Diet-therapy, Chylosa Ascites

Citation

Campos Martín C, Fernández-Argüelles García A, Rabat Restrepo JM, Sendón Pérez A. Dietoterapia en paciente con linfangiectasia intestinal primaria y ascitis quilosa de repetición. Nutr Hosp; 22(6):723-5